A Patient with Benign Lung Leiomyomatosis: Are There Any Difficulties in Diagnosis and Management?
https://doi.org/10.20514/2226-6704-2024-14-6-473-478
EDN: XFVWEA
Abstract
The article presents a clinical observation of a 48-year-old patient who applied to the Department of pulmonology in connection with accidentally detected focal formations in the lungs during a preventive examination. In the presented clinical case, the patient’s disease was asymptomatic for a long time, for the first time, focal formations in the lungs were identified in 2020 and only a year later non-specific symptoms joined. Despite multiple consultations with narrow-profile specialists and the implementation of visualization methods of examination, the diagnosis of «lung leiomyomatosis» was made only four years later after a three-fold revision of histological blocks and the exclusion of other causes of focal pulmonary dissemination. This clinical case demonstrates a rare pathology and the complexity of differential diagnosis that doctors of all specialties may encounter. The features of the disease and the complexity of differential diagnosis determine the necessity of a multidisciplinary approach to the treatment of patients with this pathology.
Keywords
leumiomatos pulmonary,
leiomyomatosis of lungs and uterus,
metastases,
lung,
rare diseases,
diagnosis
Supporting agencies: The authors declare no funding for this study
About the Authors
O. A. Kirnosova
Saratov State Medical University named after V.I. Razumovsky, Ministry of Health of the Russian Federation
Russian Federation
Competing Interests:
Russian Federation
Olga A. Kirnosova, First-year resident physician
Faculty of Medicine; Department of Hospital Therapy
Saratov
Competing Interests:
The authors declare no conflict of interests
N. A. Karoli
Saratov State Medical University named after V.I. Razumovsky, Ministry of Health of the Russian Federation
Russian Federation
Competing Interests:
Russian Federation
Nina A. Karoli, Doctor of Medical Sciences, Professor
Faculty of Medicine; Department of Hospital Therapy
Saratov
Competing Interests:
The authors declare no conflict of interests
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For citations:
Kirnosova O.A., Karoli N.A. A Patient with Benign Lung Leiomyomatosis: Are There Any Difficulties in Diagnosis and Management? The Russian Archives of Internal Medicine. 2024;14(6):473-478. https://doi.org/10.20514/2226-6704-2024-14-6-473-478. EDN: XFVWEA
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