POLYCYTHEMIA VERA IDENTIFIED IN A PATIENT WITH RESTENOSIS OF THE SUPERFICIAL FEMORAL ARTERY. CLINICAL CASE AND REVIEW OF THE LITERATURE

The article describes the clinical case of the first revealed vera polycythemia in a 67-year-old man admitted to a hospital in the hematological department of the Republican Clinical Hospital named after. G.G. Kuvatov, Ufa, about the restenosis of the superficial femoral artery. On admission, the patient’s main complaints were pain in the left leg, shortness of breath with physical exertion, headache, unstable blood pressure, numbness of hands, fatigue, general weakness. In addition, the patient was troubled by severe itching. When entering the objective status of the patient, attention was drawn to the hyperemia of the face and neck, injection of sclera, acrocyanosis, cyanotic shade of the oral mucosa, amputation stump of the lower left third of the thigh, necrotic area on the skin of the distal part of the middle finger of the right leg. After receiving laboratory and clinical data, as well as on the basis of patient complaints, a history of the disease and a clinical picture, the final clinical diagnosis was established: the vera polycythemia II B stage. Against the background of ongoing therapy, the patient noted improvement in general condition, stabilization of blood pressure, reduction of pain in the right leg, reduction of dyspnea, itching of the skin, improvement of sensitivity in the hands. According to laboratory data, positive dynamics was also revealed. This clinical observation emphasizes the need for timely diagnosis and continuous monitoring of the treatment of vera polycythemia with the help of clinical and laboratory-instrumental research methods, which is a prerequisite for correct prognosis of the course of the disease and for achieving maximum effectiveness of the therapy.

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